Arterial switch operation in patients with taussig bing. Late outcomes after arterial switch operation for taussig. Taussigbing anomaly is a rare congenital heart malformation and is one of the variants of double outlet right ventricle it consists of transposition of the aorta to the right ventricle and malposition of the pulmonary artery with subpulmonary ventricular septal defect history and etymology. Taussigbing anomaly transposition of the great arteries arterial switch operation left ventricular. In the type called the taussig bing anomaly top right diagram 2 blood from the lv passes through the vsd to the pulmonary artery, whilst blood from the rv tends to be directed mainly to the aorta. Quantitative anatomy of taussigbing anomaly longdom. When a baby is still in the womb, something goes wrong during the formation of the heart and both great arteries are attached to the right ventricle. Singlestage neonatal repair of taussigbing anomaly. Arterial switch operation in patients with taussigbing anomaly.
This report contributes significantly to the aggregate surgical experience with this uncommon disease and. Although substantial improvement has since been achieved in surgical results of the repair of the anomaly, management of the taussigbing anomaly remains challenging. Taussigbing anomaly is a rare congenital heart malformation that was first described in 1949 by helen b. Taussigbing syndrome is a cyanotic congenital heart defect in which the patient has both double outlet right ventricle dorv and subpulmonic ventricular septal defect vsd in dorv, instead of the normal situation where blood from the left ventricle lv flows out to the aorta and blood from the right ventricle rv flows out to the pulmonary artery, both aorta and pulmonary artery are. This is similar in many ways to transposition with a vsd and it may be treated with an arterial switch operation along with a patch within the. Anatomic correction of doubleoutlet right ventricle with. The heart of a neonate with the taussigbing anomaly.
The internet journal of thoracic and cardiovascular surgery. Taussigbing anomaly and coarctation of the aorta in infancy. Between january 1995 and december 2014, 9 consecutive patients who underwent aso for tga or taussigbing anomaly were. Research of taussigbing anomaly has been linked to transposition of great vessels, double outlet right ventricle, ventricular septal defects, heart septal defects, congenital heart defects. We present successful procedures for 2 infants who had the taussigbing anomaly with subaortic stenosis and coarctation of the aorta. Median age at arterial switch operation was 7 range, 2192 days, and median operative weight was 3. For a layman double outlet right ventricle is a congenital heart defect. Double root switch repair for taussigbing anomaly glaucio. Taussigbing is one of the variants of the double outlet right ventricle. Between 1983 and 1994, 20 children underwent intracardiac repair of taussig bing anomaly. Taussigbing syndrome is a cyanotic congenital heart defect chd in which the patient has both double outlet right ventricle dorv and subpulmonic ventricular septal defect vsd in dorv, instead of the normal situation where blood from the left ventricle lv flows out to the aorta and. Taussigbing syndrome synonyms, taussigbing syndrome. The journal of thoracic and cardiovascular surgery.
From 20 to 2015, 4 patients were presented with taussig bing anomaly. The article in this issue of the journal by vergnat and colleagues reports the largest singleinstitution experience with the surgical treatment of doubleoutlet right ventricle dorv with subpulmonary ventricular septal defect vsd, also known as the taussigbing anomaly. Taussingbing anomaly, with or without aortic archobstruction, can be repaired with arterial switch operation during theneonatal period with good outcome. Pdf download for double root switch repair for taussigbing. Lv blood into adjascent pa by vertically positioned infundibular septum. The diagnosis of doubleoutlet right ventricle dorv characterizes a complex heterogeneous group of congenital cardiac malformations for which multiple classification schemes have been used. The double root switch was used to repair a taussigbing anomaly in a. Pulmonary root translocation for repair of taussigbing.
Taussig bing is one of the variants of the double outlet right ventricle. Abstract seven patients with doubleoutlet right ven tricle and subpulmonary ventricular septal defect the. Staged biventricular repair of taussigbing anomaly with. Taussigbing disease definition of taussigbing disease. The characteristic feature of the taussig bing anomaly tba that makes. We conclude that twostaged arterial switch operation of taussigbing anomaly with dtransposition can be performed with low mortality, but there seems to be some risk of the compression of the left coronary artery in the original jatene method for taussigbing anomaly with sidebyside great vessels. In 1950, the similar case was reported, and the anomaly was eventually named the taussig bing heart 2. Among four, one patient had taussig bing anomaly and coarctation of aorta with 1 left circumflex and 2 right sided coronary artery, another had intramural origin of right coronary artery and left coronary artery, both of which were arising from left facing sinus. Surgical results of arterial switch operation for taussig. Results of arterial switch operation for primary total. This study identifies the impact of the position of the great arteries and use of a staged surgical approach on the outcome after the arterial switch operation in children with taussig bing anomaly. The term taussigbing anomaly was defined by stellin and colleagues to describe a spectrum of anomalies.
The surgical anatomy of the taussigbing malformation. Between 1983 and 1994, 20 children under went intracardiac repair of taussig bing anomaly. Tcell lymphoma, cutaneous other than mycosis fungoides tdp. This concept was applied in practice as a procedure known. This report contributes significantly to the aggregate surgical experience with this uncommon disease and continues. Current expectations of the arterial switch operation in a. Mmcts singlestage repair of taussigbing anomaly and. Taussig bing anomaly named after the authors that first described it helen b.
Arterial switch operation in patients with taussig bing anomaly influence of staged repair and coronary anatomy on outcome. Methods and results a retrospective study was performed, and 43 patients with taussigbing anomaly were identified between 1990 and 2011. The surgical repair of taussigbing anomaly and associated lesions has evolved over the years from palliative procedures to complete repairs either in two stages or in one single stage. Taussigbing anomaly, transposition of the great arteries, arterial switch operation, left. Frequently, associated anomalies such as aortic coarctation, arch hypoplasia, subaortic obstruction, and atypical coronary artery anatomy are present. Taussigbing heart although the anomaly was presented schematically fig. But arterial switch operation and closure of the vsd is the most widely used procedure. From 1986 through july 2005, 34 patients with taussig bing anomaly underwent the arterial switch operation.
Taussigbing anomaly is a rare congenital cardiac malformation, first described in 1949 by helen b. The taussigbing anomaly is the second most common type of doubleoutlet right ventricle. There is no consensus as to the most appropriate definition of the use of the term taussigbing malformation. Read singlestage neonatal repair of taussigbing anomaly, operative techniques in thoracic and cardiovascular surgery on deepdyve, the largest online rental service for scholarly research with thousands of academic publications available at your fingertips. The double root switch was used to repair a taussigbing anomaly in a twomonthold child.
The initial procedure was coarctoplasty and the damuskayestansel procedure with modified blalocktaussig shunt. The purpose of this paper is to delineate the morphological. Pulmonary root translocation for repair of taussig bing anomaly with interrupted arch. There are 0 terms under the parent term taussig bing syndrome in the icd10cm alphabetical index. To assess the longterm results of the arterial switch operation aso for taussigbing anomaly tba and identify risk factors affecting outcomes. This anomaly was initially described in 1949 as transposition. Taussigbing is a form of double outlet right ventricle that is characterized by the presence of subpulmonary. The second procedure was intraventricular repair kawashima procedure, damuskayestansel takedown and the reuse of native aortic and pulmonary. Late outcomes after arterial switch operation for taussigbing anomaly the journal of thoracic and cardiovascular surgery. The surgery was performed with translocation of the aortic root to the left ventricular outflow tract and the pulmonary root to the right ventricular outflow tract, after closure of the ventricular septal defect with a patch that ultimately directed flow from the left ventricle to the aorta.
Patients with taussigbing anomaly and aorticarch obstruction may have a higher reoperation rate than those with normalarch anatomy. This study identifies the impact of the position of the great arteries and use of a staged surgical approach on the outcome after the arterial switch operation in children with taussigbing anomaly. Stellin g, zuberbuhler jr, anderson rh, siewers rd. Quantitative anatomy of taussigbing anomaly leo a bockeria 1, osman a makhachev 1,2, margarita v gorgeeva 1, marina s panova 1, t atiana y u philippkina 1, titalav kh khiriev 1 and sergey b. The taussigbing anomaly should be corrected in the neonatal period or in early infancy by arterial switch operation, closure of the ventricular septal defect, and simultaneous correction of associated cardiovascular anomalies as a onestage procedure. The study of taussigbing anomaly has been mentioned in research publications which can be found using our bioinformatics tool below. Meeting abstract open access arterial switch operation. Aimsobjectives this study analyzes the impact of the position of the coronary arteries and the feasibility of staged surgical approach in children with taussig bing anomaly with aortic arch obstruction. In this study, we endorse the suggestion that the lesion be considered a spectrum of anomalies, unified by a juxtapulmonary. American pediatrician and embryologist noted for her work on congenital defects of the heart. This anomaly was initially described in 1949 as transposition of the great arteries 1. In this lecture there is description of the taussig bing syndrome as well as some of the clinical features, the diagnosis and the treatment. Crisscross heart associated with taussigbing anomaly. Author links open overlay panel hong gook lim md a jeong ryul lee md a eun jung bae md b curie ahn md c.
Mean age at operation was 17 months range, 1 week to 9 years. Taussigbing is a form of double outlet right ventricle that is characterized by the presence of subpulmonary ventricular septal defect, double conus and side by side great arteries. The characteristic feature of the taussigbing anomaly tba. The coexistence of the taussigbing anomaly and coarctation of the aorta is a highly complex situation carrying a dismal.
Synonyms for taussigbing syndrome in free thesaurus. There is doubleoutlet right ventricle with subpulmonary ventricular septal defect, double conus, and malalignment of the conal septum. Bing is a cyanotic congenital heart disease characterized by the dual presence of a subpulmonic ventricular septal defect vsd along with a double outlet right ventricle dorv. The coexistence of the taussigbing anomaly and coarctation of the aorta is a highly complex situation carrying a dismal prognosis. One of the concerns regarding the management has been the high coincidence of taussigbing anomaly with aortic arch.
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